Abstract

Ewings sarcoma /PNET are defined as round cell sarcomas that shows varying degree of neuroectodermal differentiation.ES/PNET is the second most common primary malignant tumour of bone in childhood and adolescent. The median age for patient with Ewings family of tumour is 15 years and more than 50% of the patients are adolescents. Primary malignant tumours of jaws and ES of the mandible is rare. (though more common than the maxillary involvement. Present case was mistaken as dental inflammation and resulted in delayed diagnosis.